Behcet disease combined with Sjogren syndrome
نویسندگان
چکیده
منابع مشابه
First European case of TAFRO syndrome associated with Sjogren disease
We herein describe a case of an unusual multicentric castleman disease(MCD) accompanied by Thrombocytopenia, Anasarca, myeloFibrosis and Renal failure, compatible with TAFRO syndrome and associated with Sjogren disease. The treatment with corticosteroids dramatically improved the symptoms. The clinical features of this case were similar to those reported previously in Japan but this appears to ...
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We herein present a case of a 71-year-old woman with primary Sjogren's syndrome (SjS), who developed bilateral pleural effusion and ground glass opacity during treatment with low-dose prednisolone. The pleural effusion and bronchoalveolar lavage fluid revealed elevation of lymphocytes. Thoracoscopic pleural biopsy showed infiltration of lymphocytes with no evidence of other diseases, confirming...
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By Gustavo C Roman MD (Dr. Roman, Director of the Alzheimer Center of Excellence at the Methodist Neurological Institute in Houston, Texas, has no relevant financial relationships to disclose.) Pedro J Ruiz MD (Dr. Ruiz of the California Pacific Medical Center in San Francisco, California, has no relevant financial relationships to disclose.) Originally released June 28, 2006; last updated June...
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Sjögren-Larsson syndrome is an inherited neurocutaneous disorder characterized by ichthyosis, intellectual disability, and spastic diplegia or tetraplegia. Patients have deficient activity of fatty aldehyde dehydrogenase due to mutations in the ALDH3A2 gene, which results in altered lipid composition of their tissues. In this article, the author discusses new information about the biochemical p...
متن کاملSjogren - Larsson Syndrome
Sjogren-Larsson syndrome (SLS) is an inherited disorder associated with impaired fatty alcohol oxidation due to deficient activity of fatty alcohol:NAD+ oxidoreductase (FAO). FAO is a complex enzyme which consists of two separate proteins that sequentially catalyze the oxidation of fatty alcohol to fatty aldehyde and fatty acid. To determine which enzymatic component of FAO was deficient in SLS...
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ژورنال
عنوان ژورنال: Medicine
سال: 2018
ISSN: 0025-7974
DOI: 10.1097/md.0000000000010138